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IPCCC ICD-11 Congenital Heart Atlas

You are here: Innominate artery compression syndrome Tracheo-oesophageal compressive syndrome Congenital anomaly of great arteries including arterial duct Structural developmental anomaly of heart or great vessels

IPCCC Term Innominate artery compression syndrome
IPCCC Code 09.30.23
ICD-11 Code 837654124


A congenital cardiovascular malformation in which there is anterior compression of the trachea by the innominate artery.


innominate artery compressive syndrome, brachiocephalic artery compression syndrome, brachiocephalic artery compressive syndrome, innominate artery compression of the trachea, brachiocephalic artery compression of the trachea, aberrant innominate artery, aberrant brachiocephalic artery, anomalous origin of the innominate artery, anomalous origin of the brachiocephalic artery

STS-EACTS-derived IPCCC term

Vascular ring, Innominate artery compression

EPCC-derived IPCCC term

Distal origin of innominate artery with tracheal compression (innominate artery compression syndrome)

ICD-11 MMS code or crossmap

LA8B.3*: *: This Foundation term is not in ICD-11 MMS. If using MMS to code, crossmap to higher oder term "Tracheo-oesophageal compressive syndrome" with code LA8B.3

ICD-10 MMS code or crossmap

Q25.4**: This Foundation term is not in ICD-10. Crossmap to "Other congenital malformations of aorta" with code Q25.4


Tracheo-oesophageal compressive syndrome


Coding Notes

This syndrome is a true compression of the trachea by the abnormally positioned innominate artery. The innominate artery can appear to "compress" the trachea in the presence of tracheomalacia but, in the absence of an abnormal origin and course of the innominate artery, this apparent "compression" most likely is a consequence of the tracheomalacia itself rather than actual compression by the innominate artery.

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