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IPCCC ICD-11 Congenital Heart Atlas

You are here: Congenital supravalvar mitral ring Supravalvar or intravalvar mitral ring Congenital anomaly of mitral valve Congenital anomaly of an atrioventricular valve or atrioventricular septum Structural developmental anomaly of heart or great vessels

IPCCC Term Congenital supravalvar mitral ring
IPCCC Code 06.02.17
ICD-11 MMS LA87.1Y
ICD-11 Code 308712619


A congenital cardiac malformation in which there is a fibrous shelf-like ridge of tissue located between the mitral valve and the opening to the left atrial appendage.



STS-EACTS-derived IPCCC term

Mitral valve disease, Mitral stenosis, Congenital, Supravalvar pathology, Mitral ring, Congenital supravalvar mitral ring

EPCC-derived IPCCC term

Congenital supravalvar mitral stenosis

ICD-11 MMS code or crossmap

LA87.1Y*: This Foundation term is not in ICD-11 MMS. If using MMS to code, crossmap to "Other specified congenital anomaly of mitral valve" with code LA87.1Y

ICD-10 MMS code or crossmap

Q23.8**: This term is not in ICD-10. Crossmap to higher order term: "Other congenital malformations of aortic and mitral valves"


Supravalvar or intravalvar mitral ring


Coding Notes


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