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IPCCC ICD-11 Congenital Heart Atlas

You are here: Tetralogy of Fallot with pulmonary atresia Tetralogy of Fallot Congenital right ventricular anomaly Congenital anomaly of a ventricle or the ventricular septum Structural developmental anomaly of heart or great vessels

IPCCC Term Tetralogy of Fallot with pulmonary atresia
IPCCC Code 01.01.26
ICD-11 MMS LA88.21
ICD-11 Code 1645917296


A congenital cardiovascular malformation that is a variant of tetralogy of Fallot in which there is no direct communication between the right ventricle and the pulmonary arterial tree.


Pulmonary atresia with ventricular septal defect [Fallot type]

STS-EACTS-derived IPCCC term

Tetralogy of Fallot, Pulmonary atresia

EPCC-derived IPCCC term

Tetralogy of Fallot with pulmonary atresia

ICD-11 MMS code or crossmap


ICD-10 MMS code or crossmap

**This term is not in ICD-10. If using ICD-10 to code, crossmap to higher order term “Tetralogy of Fallot”, ICD-10 code Q21.3


Tetralogy of Fallot


Coding Notes

This term should not be used when major systemic-to-pulmonary artery collaterals (including major aortopulmonary collateral arteries [MAPCAs]) are known to be present.

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