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IPCCC ICD-11 Congenital Heart Atlas

You are here: Perimembranous central ventricular septal defect Ventricular septal defect Congenital anomaly of ventricular septum Congenital anomaly of a ventricle or the ventricular septum Structural developmental anomaly of heart or great vessels

IPCCC Term Perimembranous central ventricular septal defect
IPCCC Code 07.10.01
ICD-11 MMS LA88.41
ICD-11 Code 2023258628


A congenital cardiovascular malformation in which there is a ventricular septal defect that 1) occupies the space that is usually closed by the interventricular part of the membranous septum, 2) is adjacent to the area of fibrous continuity between the leaflets of an atrioventricular valve and an arterial valve, and 3) is located at the center of the base of the ventricular mass.


Perimembranous ventricular septal defect; Membranous ventricular septal defect; Paramembranous ventricular septal defect; Type 2 ventricular septal defect; Central perimembranous ventricular septal defect

STS-EACTS-derived IPCCC term

VSD, Type 2 (Perimembranous)(Paramembranous)

EPCC-derived IPCCC term

Perimembranous central ventricular septal defect (VSD)

ICD-11 MMS code or crossmap


ICD-10 MMS code or crossmap

Q21.0**: This term is not in ICD-10. If coding using ICD-10, use the higher order term “Ventricular septal defect” with code Q21.0


Ventricular septal defect


Coding Notes

Although best used to describe the perimembranous defect that opens centrally at the base of the right ventricle, this term might be used to code perimembranous defects with inlet or outlet extension. It is recommended, however, that the more precise terms be used whenever possible for coding the latter lesions. This code is used by some as synonymous with the perimembranous, conoventricular, Type II, or the paramembranous defects. It should not be used to code an inlet VSD, or the so-called atrioventricular canal VSD. More specific terms exist for coding these entities. It is used by some to describe an isolated perimembranous VSD without extension, although it is unlikely that perimembranous defects exist in the absence of deficiency of their muscular perimeter. The conoventricular VSD with malalignment should be coded as an outlet defect, as should the perimembranous defect opening to the outlet of the right ventricle. All perimembranous defects, nonetheless, have part of their margins made up of fibrous continuity either between the leaflets of an atrioventricular and an arterial valve or, in the setting of double outlet right ventricle or overriding of the tricuspid valve, by fibrous continuity between the leaflets of the mitral and tricuspid valves. Such defects can also extend to become doubly committed and juxta-arterial (conal septal hypoplasia) when there is also fibrous continuity between the leaflets of the arterial valves or when there is a common arterial valve. Specific codes exist for these variants, which ideally should not be coded using this term.

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