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IPCCC ICD-11 Congenital Heart Atlas

You are here: Aortic valvar atresia Congenital anomaly of aortic valve Congenital anomaly of a ventriculo-arterial valve or adjacent regions Structural developmental anomaly of heart or great vessels

IPCCC Term Aortic valvar atresia
IPCCC Code 09.15.06
ICD-11 MMS LA8A.23
ICD-11 Code 1700740306


A congenital cardiovascular malformation in which there is no orifice of the aortic valve.


Aortic valve atresia, Atresia of the aortic valve, aorta valvular atresia, aortic valvular atresia, congenital aortic: atresia, congenital atresia of aortic valve, imperforate aortic valve

STS-EACTS-derived IPCCC term

Aortic atresia, Aortic valvar atresia

EPCC-derived IPCCC term

Aortic valvar atresia

ICD-11 MMS code or crossmap


ICD-10 MMS code or crossmap

Q23.0: Congenital stenosis of aortic valve (includes "Aortic atresia")


Congenital anomaly of aortic valve


Coding Notes

Aortic valve atresia will most often be coded under the hypoplastic left heart syndrome/complex diagnostic codes since it most often occurs as part of a spectrum of cardiovascular malformations. However, there is a small subset of patients with aortic valve atresia who have a well developed left ventricle and mitral valve and a large ventricular septal defect (nonrestrictive or restrictive).

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