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IPCCC ICD-11 Congenital Heart Atlas

You are here: Transposition of the great arteries with concordant atrioventricular connections and ventricular septal defect and left ventricular outflow tract obstruction Transposition of the great arteries Congenital anomaly of an atrioventricular or ventriculo-arterial connection Structural developmental anomaly of heart or great vessels

IPCCC Term Transposition of the great arteries with concordant atrioventricular connections and ventricular septal defect and left ventricular outflow tract obstruction
IPCCC Code 01.01.10+07.09.01
ICD-11 MMS LA85.1
ICD-11 Code 1744213081

Definition

A congenital cardiovascular malformation in which the morphologically right atrium connects to the morphologically right ventricle, the morphologically left atrium connects to the morphologically left ventricle, the morphologically right ventricle connects to the aorta, the morphologically left ventricle connects to the pulmonary trunk, one or more ventricular septal defects are present, and left ventricular outflow tract obstruction is present.

Synonyms/Abbreviations

Concordant atrioventricular connections and discordant ventriculo-arterial connections with ventricular septal defect and left ventricular outflow tract obstruction; Transposition with ventricular septal defect and pulmonary stenosis

STS-EACTS-derived IPCCC term

TGA - VSD - LVOTO (Transposition of the Great Arteries - Ventricular septal defect - Left ventricular outflow tract obstruction) (Concordant atrioventricular connections and Discordant ventriculo-arterial connections - VSD - LVOTO)

EPCC-derived IPCCC term

Transposition of the great arteries with concordant atrioventricular connections and ventricular septal defect + Left ventricular outflow tract obstruction

ICD-11 MMS code or crossmap

LA85.1*: This Foundation term is not in ICD-11 MMS. If  using ICD-11MMS to code, crossmap to higher order term “Transposition of the great arteries”, ICD-11 MMS code LA85.1

ICD-10 MMS code or crossmap

Q20.3**: This term is not in ICD-10. If  using ICD-10 to code, crossmap to higher order term “Discordant ventriculoarterial connection”, with code Q20.3

Parent

Transposition of the great arteries

Siblings

Coding Notes

The stand-alone term "Left ventricular outflow tract obstruction" (with IPCCC code 07.09.01) exists only in the diagnostic long list of the IPCCC, and does not appear as an isolated term in the ICD Foundation list. The term "Congenital left ventricular outflow tract obstruction" does exist in ICD-11 (entity #567908339) and the IPCCC short and long lists with #07.09.28.