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IPCCC ICD-11 Congenital Heart Atlas

You are here: Congenital aortic valvar stenosis Congenital anomaly of aortic valve Congenital anomaly of a ventriculo-arterial valve or adjacent regions Structural developmental anomaly of heart or great vessels

IPCCC Term Congenital aortic valvar stenosis
IPCCC Code 09.15.01
ICD-11 MMS LA8A.20
ICD-11 Code 1824398514


A congenital cardiovascular malformation of the aortic valve in which there is narrowing or stricture (obstruction to flow). ‘Congenital aortic valvar stenosis’ arises most commonly as a result of partial or complete fusion of one or more commissures, or is due to dysplasia of one or more aortic cusps. These congenital malformations of the aortic valve may not be initially obstructive but may become stenotic later in life due to leaflet thickening, poor relative growth and-or calcification. It is not until the congenitally malformed aortic valve is or becomes stenotic that this term should be used.


Congenital valvar aortic stenosis; Congenital valvular aortic stenosis; Congenital aortic valve stricture; Congenital stenosis of aortic valve; Congenital aortic valve stenosis

STS-EACTS-derived IPCCC term

Aortic stenosis, Valvar, Congenital

EPCC-derived IPCCC term

Congenital aortic valvar stenosis

ICD-11 MMS code or crossmap


ICD-10 MMS code or crossmap

Q23.0: Congenital stenosis of aortic valve (includes "Aortic atresia")


Congenital anomaly of aortic valve


Coding Notes


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