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IPCCC ICD-11 Congenital Heart Atlas

You are here: Right ventricular hypoplasia Congenital right ventricular anomaly Congenital anomaly of a ventricle or the ventricular septum Structural developmental anomaly of heart or great vessels

IPCCC Term Right ventricular hypoplasia
IPCCC Code 07.02.00
ICD-11 Code 2088837187


A congenital cardiac malformation in which the right ventricle is abnormally small (below the lower limit of normal adjusted for body size).


Hypoplastic right ventricle

STS-EACTS-derived IPCCC term

Hypoplastic right ventricle

EPCC-derived IPCCC term

Right ventricular hypoplasia

ICD-11 MMS code or crossmap

LA88.Y*: This Foundation term is not in ICD-11 MMS. If coding in MMS use term “Other specified congenital anomaly of a ventricle or the ventricular septum” with code LA88.Y

ICD-10 MMS code or crossmap

Q20.8**: This Foundation term is not in ICD-10. If using ICD-10 to code, crossmap to higher order term "Other congenital malformations of cardiac chambers or connections" with code Q20.8


Congenital right ventricular anomaly


Coding Notes

This morphological abnormality usually is an integral part of other congenital cardiovascular anomalies and, therefore, frequently does not need to be coded separately. It should, however, be coded as secondary to an accompanying congenital cardiovascular anomaly if the right ventricular hypoplasia is not considered an integral and understood part of the primary congenital cardiovascular diagnosis. It would rarely be coded as a primary and/or isolated diagnosis.

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