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IPCCC ICD-11 Congenital Heart Atlas

You are here: Atrioventricular septal defect and tetralogy of Fallot Common atrioventricular junction with atrioventricular septal defect Common atrioventricular junction Congenital anomaly of an atrioventricular valve or atrioventricular septum Structural developmental anomaly of heart or great vessels

IPCCC Term Atrioventricular septal defect and tetralogy of Fallot
IPCCC Code 01.01.20
ICD-11 MMS LA87.2Y
ICD-11 Code 915281294

Definition

A congenital cardiac malformation with both an atrioventricular septal defect (atrioventricular canal defect) and tetralogy of Fallot.

Synonyms/Abbreviations

  • Atrioventricular septal defect associated with tetralogy of Fallot
  • Atrioventricular canal and Tetralogy of Fallot

STS-EACTS-derived IPCCC term

Tetralogy of Fallot, Common atrioventricular canal (AVSD)

EPCC-derived IPCCC term

Atrioventricular septal defect and Tetralogy of Fallot

ICD-11 MMS code or crossmap

LA87.45

ICD-10 MMS code or crossmap

Q21.2 and Q21.3**: This Foundation term is not in ICD-10. If using ICD-10 to code, crossmap to higher order terms “Atrioventricular septal defect”, ICD-10 code Q21.2, and "Tetralogy of Fallot", ICD-10 code Q21.3

Parent

Common atrioventricular junction with atrioventricular septal defect

Siblings

Coding Notes

Tetralogy of Fallot with atrioventricular septal defect (common atrioventricular canal) is always the complete form (unrestrictive interventricular component) and usuallyhas four leaflets of the common atrioventricular valve (undivided superior leaflet) and very few or no attachments of that leaflet to the crest of the ventricular septum.