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IPCCC ICD-11 Congenital Heart Atlas

You are here: Double aortic arch Vascular Ring Congenital anomaly of great arteries including arterial duct Structural developmental anomaly of heart or great vessels

IPCCC Term Double aortic arch
IPCCC Code 09.28.09
ICD-11 Code 960436403


A congenital cardiovascular malformation in which the right and left aortic arches (patent or atretic) encircle the trachea and oesophagus.


Encircling double aortic arch

STS-EACTS-derived IPCCC term

Vascular ring, Double aortic arch

EPCC-derived IPCCC term

Double aortic arch

ICD-11 MMS code or crossmap

LA8B.Y*: This Foundation term is not in ICD-11 MMS. If coding in MMS, crossmap to higher order MMS term "Other specified congenital anomaly of great arteries including arterial duct" with code LA8B.Y

ICD-10 MMS code or crossmap

Q25.4: Other congenital malformations of aorta (which includes Double aortic arch)


Vascular Ring


Coding Notes


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