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IPCCC ICD-11 Congenital Heart Atlas

You are here: Left ventricular hypoplasia Congenital left ventricular anomaly Congenital anomaly of a ventricle or the ventricular septum Structural developmental anomaly of heart or great vessels

IPCCC Term Left ventricular hypoplasia
IPCCC Code 07.07.00
ICD-11 MMS L88.Y
ICD-11 Code 1353575853


A congenital cardiac malformation in which the left ventricle is abnormally small (below the lower limit of normal adjusted for body size).


Hypoplastic left ventricle

STS-EACTS-derived IPCCC term

Hypoplastic left ventricle

EPCC-derived IPCCC term

Left ventricular hypoplasia

ICD-11 MMS code or crossmap

LA88.Y*: This Foundation term is not in ICD-11 MMS. If coding in MMS use term “Other specified congenital anomaly of a ventricle or the ventricular septum” with code LA88.Y

ICD-10 MMS code or crossmap

Q20.8**: This Foundation term is not in ICD-10. If using ICD-10 to code, crossmap to higher order term "Other congenital malformations of cardiac chambers or connections" with code Q20.8


Congenital left ventricular anomaly


Coding Notes

This morphological abnormality usually is an integral part of other congenital cardiovascular anomalies and does not need to be coded separately if this is the case. It should be coded as secondary to an accompanying congenital cardiovascular anomaly if the left ventricular hypoplasia is not considered an integral and understood part of the primary congenital cardiovascular diagnosis such as hypoplastic left heart syndrome.

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