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IPCCC ICD-11 Congenital Heart Atlas

You are here: Mitral annular hypoplasia Congenital anomaly of mitral valve Congenital anomaly of an atrioventricular valve or atrioventricular septum Structural developmental anomaly of heart or great vessels

IPCCC Term Mitral annular hypoplasia
IPCCC Code 06.02.04
ICD-11 MMS LA87.1Y
ICD-11 Code 843702959


A congenital cardiac malformation of the mitral valve in which there is annular hypoplasia (incomplete development or underdevelopment so that it is abnormally small [below the lower limit of normal adjusted for body size]). Hypoplasia may or may not be associated with stenosis.


Hypoplasia of mitral valvar annulus; Hypoplasia of the mitral annulus

STS-EACTS-derived IPCCC term

Mitral valve disease, Mitral valve pathology, Mitral valve annulus hypoplasia

EPCC-derived IPCCC term

Mitral annular hypoplasia

ICD-11 MMS code or crossmap

LA87.1Y*: This Foundation term is not in ICD-11 MMS. If using MMS to code, crossmap to "Other specified congenital anomaly of mitral valve" with code LA87.1Y

ICD-10 MMS code or crossmap

Q23.8**: This term is not in ICD-10. Crossmap to higher order term: "Other congenital malformations of aortic and mitral valves"


Congenital anomaly of mitral valve


Coding Notes


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