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IPCCC ICD-11 Congenital Heart Atlas

You are here: Doubly committed juxta-arterial ventricular septal defect with anteriorly malaligned fibrous outlet septum and perimembranous extension Doubly committed juxta-arterial ventricular septal defect with anteriorly malaligned fibrous outlet septum Outlet ventricular septal defect with anteriorly malaligned outlet septum Outlet ventricular septal defect Ventricular septal defect Congenital anomaly of ventricular septum Congenital anomaly of a ventricle or the ventricular septum Structural developmental anomaly of heart or great vessels

IPCCC Term Doubly committed juxta-arterial ventricular septal defect with anteriorly malaligned fibrous outlet septum and perimembranous extension
IPCCC Code 07.12.05
ICD-11 MMS LA88.4Y
ICD-11 Code 1496410457

Definition

A congenital cardiac malformation in which there is an outlet ventricular septal defect with perimembranous extension, bordered superiorly by the area of fibrous continuity or a fibrous outlet septum between the aortic and pulmonary valves, and the fibrous outlet septum is malaligned in an antero-cranial fashion with respect to the trabecular muscular septum such that there is overriding of the arterial valve supported predominantly by the left ventricle.

Synonyms/Abbreviations

Doubly committed subarterial ventricular septal defect with perimembranous extension and anterior malalignment of outlet septum; Doubly committed juxta-arterial ventricular septal defect with anteriorly malaligned fibrous outlet septum and fibrous postero-inferior rim (perimembranous)

STS-EACTS-derived IPCCC term

VSD, Type 1 (Subarterial) (Supracristal) (Conal septal defect) (Infundibular), Juxtaarterial, Doubly committed, With membranous septum extension (Conal septal hypoplasia without cranial muscular border and with perimembranous extension), With anteriorly malaligned fibrous outlet septum

EPCC-derived IPCCC term

Doubly committed juxta-arterial ventricular septal defect (VSD) with anteriorly malaligned fibrous outlet septum and perimembranous extension

ICD-11 MMS code or crossmap

LA88.4Y*: This ICD-11 Foundation term is not in ICD-11MMS. If using ICD-11MMS to code for this term, crossmap to the higher order term Other specified ventricular septal defect with code LA88.4Y

ICD-10 MMS code or crossmap

Q21.0**: This term is not in ICD-10. If coding using ICD-10, use the higher order term Ventricular septal defect with code Q21.0

Parent

Doubly committed juxta-arterial ventricular septal defect with anteriorly malaligned fibrous outlet septum

Siblings

Coding Notes

None