If you have feedback, let us know.

IPCCC ICD-11 Congenital Heart Atlas

You are here: Congenital subaortic stenosis Congenital anomaly of a ventriculo-arterial valve or adjacent regions Structural developmental anomaly of heart or great vessels

IPCCC Term Congenital subaortic stenosis
IPCCC Code 07.09.50
ICD-11 Code 1350872731


A congenital cardiovascular malformation associated with narrowing within the outflow tract supporting the aortic valve.


Congenital subvalvular aortic stenosis; Subvalvular aortic stenosis, Congenital; Congenital subvalvar aortic stenosis

STS-EACTS-derived IPCCC term

Aortic stenosis, Subvalvar, Congenital subaortic stenosis

EPCC-derived IPCCC term

Congenital subaortic stenosis

ICD-11 MMS code or crossmap


ICD-10 MMS code or crossmap

Q24.4: Congenital subaortic stenosis


Congenital anomaly of a ventriculo-arterial valve or adjacent regions



Coding Notes

This term should be used for congenital subaortic stenosis due to lesions such as deviation of the outlet septum (seen in coarctation of the aorta and interrupted aortic arch), or a restrictive ventricular septal defect (bulboventricular foramen) in single ventricle complexes. This term should not be used for subaortic stenosis due to a fibromuscular shelf or tunnel, as specific terms exist for these lesions. For subaortic stenosis due to an atrioventricular valve in the setting of normal ventriculo-arterial connections, the term ‘Congenital left ventricular outflow tract obstruction due to an atrioventricular valve’ should be used.

© Copyright - ISNPCHD - Developed and supported by Becker Associates, a Canadian Association Management Company