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IPCCC ICD-11 Congenital Heart Atlas

You are here: Congenital pulmonary valvar atresia Congenital pulmonary atresia Congenital anomaly of a ventriculo-arterial valve or adjacent regions Structural developmental anomaly of heart or great vessels

IPCCC Term Congenital pulmonary valvar atresia
IPCCC Code 09.05.12
ICD-11 Code 2133636301


A congenital cardiac malformation in which the pulmonary valve leaflet structure is present but imperforate.


Congenital pulmonary valve atresia; Imperforate pulmonary valve; Pulmonary valvar atresia; Atretic pulmonary valve; Pulmonary valvular atresia.

STS-EACTS-derived IPCCC term

Pulmonary atresia, Congenital, Congenital pulmonary valvar atresia

EPCC-derived IPCCC term

Pulmonary atresia: imperforate valve

ICD-11 MMS code or crossmap

LA8A.1Y*: This Foundation term is not in ICD-11 MMS. If using MMS to code, crossmap to "Other specified congenital pulmonary atresia" with code LA8A.1Y

ICD-10 MMS code or crossmap

Q22.0: Congenital pulmonary valve atresia


Congenital pulmonary atresia


Coding Notes

This term is limited to describe hearts in which the pulmonary subvalvar or supravalvar regions are not atretic.