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IPCCC ICD-11 Congenital Heart Atlas

You are here: Pulmonary arteriovenous fistula Structural developmental anomaly of heart or great vessels

IPCCC Term Pulmonary arteriovenous fistula
IPCCC Code 09.19.05
ICD-11 MMS LA90.5
ICD-11 Code 913404991


A congenital cardiovascular malformation in which there is an abnormal, direct connection between a pulmonary artery and pulmonary vein or left atrium without an intervening capillary bed.


Pulmonary arteriovenous malformation; Pulmonary arteriovenous aneurysm

STS-EACTS-derived IPCCC term

Pulmonary AV fistula[s] (Pulmonary arteriovenous malformation[s] [AVM]), Congenital

EPCC-derived IPCCC term

Pulmonary arteriovenous fistula (malformation)

ICD-11 MMS code or crossmap


ICD-10 MMS code or crossmap

Q25.7**: This Foundation term is not in ICD-10. If using ICD-10 to code, crossmap to higher order term "Other congenital malformations of pulmonary artery" with code Q25.7


Structural developmental anomaly of heart or great vessels


Coding Notes