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IPCCC ICD-11 Congenital Heart Atlas

You are here: Extrathoracic heart Anomalous position-orientation of heart Congenital anomaly of position or spatial relationships of thoraco-abdominal organs Structural developmental anomaly of heart or great vessels

IPCCC Term Extrathoracic heart
IPCCC Code 02.01.01
ICD-11 MMS LA80.3
ICD-11 Code 285576893


A congenital cardiovascular malformation in which the heart is at least partially outside of the thorax.


Ectopia cordis

STS-EACTS-derived IPCCC term

Ectopia cordis

EPCC-derived IPCCC term

Extrathoracic heart (ectopia cordis)

ICD-11 MMS code or crossmap


ICD-10 MMS code or crossmap

Q24.8**: This term is not in ICD-10. If using ICD-10 to code this term, crossmap to higher order term “Other specified congenital malformations of heart” with code Q24.8


Anomalous position-orientation of heart


Coding Notes