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IPCCC ICD-11 Congenital Heart Atlas

You are here: Congenital aortopulmonary window Congenital anomaly of great arteries including arterial duct Structural developmental anomaly of heart or great vessels

IPCCC Term Congenital aortopulmonary window
IPCCC Code 09.04.07
ICD-11 Code 1988278118


A congenital cardiovascular malformation in which there is side-to-side continuity of the lumens of the ascending aorta and pulmonary trunk in association with separate aortic and pulmonary valves or their atretic remnants.


Aortopulmonary window; Aortic septal defect; Aortopulmonary septal defect; aorticopulmonary window; aorticopulmonary fenestration; aorticopulmonary septal defect

STS-EACTS-derived IPCCC term

AP window (aortopulmonary window), Congenital aortopulmonary window

EPCC-derived IPCCC term

Congenital aortopulmonary window

ICD-11 MMS code or crossmap


ICD-10 MMS code or crossmap

Q21.4: Aortopulmonary septal defect (includes "Aortopulmonary window")


Congenital anomaly of great arteries including arterial duct


Coding Notes

Side-to-side continuity of the lumens of the aorta and pulmonary arterial tree, which is distinguished from common arterial trunk (truncus arteriosus) by the presence of two arterial valves or their atretic remnants, and involvement of the pulmonary trunk (main pulmonary artery).