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IPCCC ICD-11 Congenital Heart Atlas

You are here: Congenital pulmonary venous stenosis or hypoplasia Congenital anomaly of pulmonary vein Congenital anomaly of mediastinal vein Structural developmental anomaly of heart or great vessels

IPCCC Term Congenital pulmonary venous stenosis or hypoplasia
IPCCC Code 04.08.31
ICD-11 MMS LA86.3
ICD-11 Code 469101490


A congenital cardiovascular malformation with a pathologic narrowing of one or more pulmonary veins including diffuse hypoplasia, long segment focal/tubular stenosis and/or discrete stenosis.


Congenital pulmonary vein stenosis and/or hypoplasia

STS-EACTS-derived IPCCC term

Pulmonary venous stenosis and/or hypoplasia, Congenital

EPCC-derived IPCCC term

Congenital pulmonary venous stenosis and-or hypoplasia

ICD-11 MMS code or crossmap


ICD-10 MMS code or crossmap

Q26.8**: This Foundation term is not in ICD-10. If using ICD-10 to code, crossmap to "Other congenital malformation of great veins" with code Q26.8


Congenital anomaly of pulmonary vein


Coding Notes


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