If you have feedback, let us know.

IPCCC ICD-11 Congenital Heart Atlas

You are here: Tetralogy of Fallot Congenital right ventricular anomaly Congenital anomaly of a ventricle or the ventricular septum Structural developmental anomaly of heart or great vessels

IPCCC Term Tetralogy of Fallot
IPCCC Code 01.01.01
ICD-11 MMS LA88.2
ICD-11 Code 90973426


A group of congenital cardiac malformations with biventricular atrioventricular alignments or connections characterized by anterosuperior deviation of the conal or outlet septum or its fibrous remnant, narrowing or atresia of the pulmonary outflow, a ventricular septal defect of the malalignment type, and biventricular origin of the aorta. Tetralogy of Fallot will always have a ventricular septal defect, narrowing or atresia of the pulmonary outflow, aortic override, and most often right ventricular hypertrophy.


Tetrad of Fallot; Fallot tetralogy; Fallot tetrad; Fallot disease; Fallot complex; Fallot's tetralogy; Subpulmonic stenosis, ventricular septal defect, overriding aorta, and right ventricular hypertrophy; Ventricular septal defect with pulmonary stenosis or atresia, dextroposition of aorta, and hypertrophy of right ventricle

STS-EACTS-derived IPCCC term

Tetralogy of Fallot

EPCC-derived IPCCC term

Tetralogy of Fallot

ICD-11 MMS code or crossmap


ICD-10 MMS code or crossmap

Q21.3: Tetralogy of Fallot


Congenital right ventricular anomaly



Coding Notes


© Copyright - ISNPCHD - Developed and supported by Becker Associates, a Canadian Association Management Company