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IPCCC ICD-11 Congenital Heart Atlas

You are here: Congenital pulmonary trunk hypoplasia Congenital pulmonary trunk anomaly Congenital anomaly of pulmonary arterial tree Congenital anomaly of great arteries including arterial duct Structural developmental anomaly of heart or great vessels

IPCCC Term Congenital pulmonary trunk hypoplasia
IPCCC Code 09.07.20
ICD-11 Code 1152699781


A congenital cardiovascular malformation of the pulmonary trunk (main pulmonary artery) in which there is incomplete development or underdevelopment resulting in diffuse luminal narrowing (below the lower limit of normal adjusted for body size).


Main pulmonary artery hypoplasia

STS-EACTS-derived IPCCC term

Pulmonary trunk (MPA) abnormality, Congenital pulmonary trunk (main pulmonary artery) hypoplasia

EPCC-derived IPCCC term

Congenital pulmonary trunk hypoplasia

ICD-11 MMS code or crossmap

LA8B.1*: This Foundation term is not in ICD-11 MMS. If using MMS to code, crossmap to higher order term "Congenital anomaly of pulmonary arterial tree" with code LA8B.1

ICD-10 MMS code or crossmap

Q25.7**: This Foundation term is not in ICD-10. If using ICD-10 to code, crossmap to higher order term "Other congenital malformations of pulmonary artery" with code Q25.7


Congenital pulmonary trunk anomaly


Coding Notes

The stenosis or hypoplasia may be isolated or associated with other cardiovascular lesions. Since the narrowing is distal to the pulmonary valve, it may also be known as supravalvar pulmonary stenosis.

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