You are here: Scimitar syndrome ⇗ Partial anomalous pulmonary venous connection of Scimitar type ⇗ Anomalous pulmonary venous connection ⇗ Congenital anomaly of pulmonary vein ⇗ Congenital anomaly of mediastinal vein ⇗ Structural developmental anomaly of heart or great vessels
|IPCCC Term||Scimitar syndrome|
A congenital cardiopulmonary malformation with “partial anomalous pulmonary venous connection of Scimitar type” and one or more of the following: hypoplasia of the right lung with bronchial anomalies, dextrocardia, hypoplasia of the right pulmonary artery, lobar lung sequestration, and anomalous systemic arterial supply to the lower lobe of the right lung directly from the aorta or its main branches.
Pulmonary venolobar syndrome
STS-EACTS-derived IPCCC term
Partial anomalous pulmonary venous connection (PAPVC), Scimitar type with Scimitar syndrome
EPCC-derived IPCCC term
ICD-11 MMS code or crossmap
ICD-10 MMS code or crossmap
Q26.8**: This Foundation term is not in ICD-10. If using ICD-10 to code, crossmap to "Other congenital malformation of great veins" with code Q26.8 which includes "Scimitar sybdrome"
Partial anomalous pulmonary venous connection of Scimitar type