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IPCCC ICD-11 Congenital Heart Atlas

You are here: Pulmonary annular hypoplasia Congenital anomaly of pulmonary valve Congenital anomaly of a ventriculo-arterial valve or adjacent regions Structural developmental anomaly of heart or great vessels

IPCCC Term Pulmonary annular hypoplasia
IPCCC Code 09.05.05
ICD-11 Code 663601170


A congenital cardiovascular malformation of the pulmonary valve in which its 'annulus' is hypoplastic (incomplete development or underdevelopment so that it is abnormally small [below the lower limit of normal adjusted for body size]).



STS-EACTS-derived IPCCC term

Pulmonary valve pathology, Pulmonary valvar 'annulus' hypoplasia

EPCC-derived IPCCC term

Pulmonary 'annular' hypoplasia

ICD-11 MMS code or crossmap

LA8A.0Y*: his Foundation term is not in ICD-11 MMS. If using MMS to code, crossmap to "Other specified congenital anomaly of pulmonary valve" with code LA8A.0Y

ICD-10 MMS code or crossmap

Q22.3**: This Foundation term is not in ICD-10. Crossmap to higher order term "Other congenital malformations of pulmonary valve" with code Q22.3


Congenital anomaly of pulmonary valve


Coding Notes


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