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IPCCC ICD-11 Congenital Heart Atlas

You are here: Atrioventricular septal defect with communication at the atrial level only Common atrioventricular junction with atrioventricular septal defect Common atrioventricular junction Congenital anomaly of an atrioventricular valve or atrioventricular septum Structural developmental anomaly of heart or great vessels

IPCCC Term Atrioventricular septal defect with communication at the atrial level only
IPCCC Code 06.06.01
ICD-11 MMS LA87.21
ICD-11 Code 1159570489

Definition

A congenital cardiac malformation that is a variant of an atrioventricular septal defect (atrioventricular canal defect) with an interatrial communication just above the atrioventricular valve, no interventricular communication just below the atrioventricular valve, separate right and left atrioventricular valvar orifices, and varying degrees of malformation of the left-sided component of the common atrioventricular valve. The bridging leaflets of the common atrioventricular valve are bound down to the crest of the scooped-out ventricular septum so that the potential for shunting through the atrioventricular septal defect is possible only at the atrial level and not at the ventricular level.

Synonyms/Abbreviations

Atrioventricular septal defect with atrial shunting only
Primum atrial septal defect
Persistent ostium primum
Partial atrioventricular septal defect, ostium primum type
Partial atrioventricular canal defect with isolated atrial component
Partial atrioventricular canal defect
Partial atrioventricular septal defect
Ostium primum atrial septal defect
Incomplete atrioventricular septal defect with isolated atrial component
Incomplete atrioventricular canal defect with isolated atrial component

STS-EACTS-derived IPCCC term

AVC (AVSD), Partial (incomplete) (PAVSD) (ASD primum with no VSD)

EPCC-derived IPCCC term

Atrioventricular septal defect with communication at the atrial level only (primum atrial septal defect) (partial atrioventricular canal defect)

ICD-11 MMS code or crossmap

LA87.40

ICD-10 MMS code or crossmap

Q21.2: Atrioventricular septal defect (includes "Ostium primum atrial septal defect - type I")

Parent

Common atrioventricular junction with atrioventricular septal defect

Siblings

Coding Notes

None

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