Entries by ISNPCHD Admin

06.01.34 – Ebstein malformation of tricuspid valve

IPCCC Term EBSTEIN MALFORMATION OF TRICUSPID VALVE IPCCC Code 06.01.34 ICD-11 Code PENDING Synonyms PENDING Abbreviations PENDING IPCCC Definition A congenital cardiac malformation of the tricuspid valve and right ventricle that is characterized by downward (apical) displacement of the functional annulus, usually involving the septal and inferior (posterior) leaflets.

01.01.03 – Congenitally corrected transposition of great arteries

IPCCC Term CONGENITALLY CORRECTED TRANSPOSITION OF GREAT ARTERIES IPCCC Code 01.01.03 ICD-11 Code PENDING Synonyms PENDING Abbreviations PENDING IPCCC Definition A congenital cardiovascular malformation in which the morphologically right atrium connects to the morphologically left ventricle, the morphologically left atrium connects to the morphologically right ventricle, the morphologically right ventricle connects to the aorta, and […]

09.04.07 – Congenital aortopulmonary window

IPCCC Term CONGENITAL AORTOPULMONARY WINDOW IPCCC Code 09.04.07 ICD-11 Code PENDING Synonyms PENDING Abbreviations PENDING IPCCC Definition A congenital cardiovascular malformation in which there is side-to-side continuity of the lumens of the ascending aorta and pulmonary trunk in association with separate aortic and pulmonary valves or their atretic remnants.

05.01.02 – Atrial septal defect within oval fossa

IPCCC Term ATRIAL SEPTAL DEFECT WITHIN OVAL FOSSA IPCCC Code 05.01.02 ICD-11 Code PENDING Synonyms PENDING Abbreviations PENDING IPCCC Definition A congenital cardiac malformation in which there is an interatrial communication confined to the region of the oval fossa (fossa ovalis), most commonly due to a deficiency of the primary atrial septum (septum primum) but […]

09.02.01 – Dysplasia of truncal valve

IPCCC Term DYSPLASIA OF TRUNCAL VALVE IPCCC Code 09.02.01 ICD-11 Code PENDING Synonyms PENDING Abbreviations PENDING IPCCC Definition A congenital cardiovascular malformation where the truncal valve leaflets are markedly thickened with restricted mobility, characterized by the presence of myxomatous tissue.

09.01.14 – Common arterial trunk with aortic dominance and both pulmonary arteries arising from trunk

IPCCC Term COMMON ARTERIAL TRUNK WITH AORTIC DOMINANCE AND BOTH PULMONARY ARTERIES ARISING FROM TRUNK IPCCC Code 09.01.14 ICD-11 Code PENDING Synonyms PENDING Abbreviations PENDING IPCCC Definition A congenital cardiovascular malformation in which a common arterial trunk is associated with an unobstructed aortic arch and both pulmonary arteries arise from the common arterial trunk.

09.01.01 – Common arterial trunk

IPCCC Term COMMON ARTERIAL TRUNK IPCCC Code 09.01.01 ICD-11 Code PENDING Synonyms PENDING Abbreviations PENDING IPCCC Definition A congenital cardiovascular malformation in which a single arterial trunk arises from the heart, giving origin sequentially to the coronary arteries, one or more pulmonary arteries, and the systemic arterial circulation.