09.45.10 – Congenital coronary arterial fistula to right ventricle

IPCCC Term CONGENITAL CORONARY ARTERIAL FISTULA TO RIGHT VENTRICLE

IPCCC Code 09.45.10

ICD-11 Code PENDING

Synonyms PENDING

Abbreviations PENDING

IPCCC Definition A congenital cardiovascular malformation in which a coronary artery communicates, through an anomalous channel, with the right ventricle.

  • Image #1: In this anterior view, the right ventricle is opened in clam-shell fashion to demonstrate a large, fistulous communication between the coronary arteries and the right ventricle (black arrows). The inferior interventricular coronary arteries both contribute to this fistulous communication. This heart demonstrates the most severe variant of pulmonary atresia with intact ventricular septum in which only the inlet component of the right ventricle is present. The apical trabecular component and the outlet have been mostly obliterated by muscular hypertrophy. Image #2: This short axis view shows the apical component of both the right and left ventricles with a large coronary artery to right ventricular fistula.
  • Content for Echocardiogram.
  • Content for Computerized Axial Tomography.
  • Content for Angiography.
  • Content for Intraoperative Videos.