IPCCC Term CONGENITAL AORTOPULMONARY WINDOW
IPCCC Code 09.04.07
ICD-11 Code PENDING
IPCCC Definition A congenital cardiovascular malformation in which there is side-to-side continuity of the lumens of the ascending aorta and pulmonary trunk in association with separate aortic and pulmonary valves or their atretic remnants.
Image #1 shows an anterior view of the normally related arterial trunks that are clearly separate as they exit the ventricular mass. The yellow star marks the outer surface of the aortopulmonary window. The brachiocephalic arteries branch normally from the aortic arch which extends to the left. Image #2 shows a similar view of the same heart with the aorta opened from just above the valve, along the ascending portion and into the arch. The aortic aspect of the aortopulmonary window is marked with yellow dots. The right pulmonary artery can be seen through the aortopulmonary window. Image #3 shows the opened right ventricular outflow tract, pulmonary valve and pulmonary trunk from the same heart shown in the other panels. The pulmonary aspect of the aortopulmonary window is marked with yellow dots and lies between the valve and the bifurcation of the left pulmonary artery.
- Content for Echocardiogram.
- Content for Computerized Axial Tomography.
- Content for Angiography.
- Content for Intraoperative Videos.