IPCCC Term CONGENITAL ANOMALY OF LEFT-SIDED ATRIOVENTRICULAR VALVE IN DOUBLE INLET VENTRICLE
IPCCC Code 06.04.11
ICD-11 Code PENDING
IPCCC Definition A congenital cardiac malformation in association with double inlet ventricle (excluding common atrioventricular valve) in which the atrioventricular valve morphology cannot be determined. This term should be usedÂ for the left-sided atrioventricular valve in those hearts.
This heart is viewed from posterior to anterior and has been cut in a four chamber echocardiographic plane. There is a double inlet left ventricle with an abnormality of the left-sided atrioventricular valve. It straddles the interventricular septum with the tension apparatus extending across the ventricular septal defect into the rudimentary, incomplete right ventricle. This heart was explanted following a Fontan procedure. Note the remnant of the right-sided atrial baffle (red star).
- Content for Echocardiogram
- Content for Computerized Axial Tomography
- Content for Angiography
- Content for Intraoperative Videos