01.01.10 – Transposition of the great arteries with concordant atrioventricular connections and ventricular septal defect

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IPCCC Term TRANSPOSITION OF THE GREAT ARTERIES WITH CONCORDANT ATRIOVENTRICULAR CONNECTIONS AND VENTRICULAR SEPTAL DEFECT

IPCCC Code 01.01.10

ICD-11 Code PENDING

Synonyms PENDING

Abbreviations PENDING

IPCCC Definition A congenital cardiovascular malformation in which the morphologically right atrium connects to the morphologically right ventricle, the morphologically left atrium connects to the morphologically left ventricle, the morphologically right ventricle connects to the aorta, the morphologically left ventricle connects to the pulmonary trunk, and one or more ventricular septal defects are present.

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01-01-10 The anterior free wall of the right atrium, right ventricle and aorta have been removed to view the septal surfaces of this heart with transposition. There are concordant atrioventricular connections and discordant ventriculo-arterial connections with the tricuspid valve guarding the inlet of the right ventricle and the aorta arising from a complete muscular infundibulum. The defect extends into the outlet component of the right ventricle and has a muscular postero-inferior border. (Red star – pulmonary trunk) There is an atrial septal defect.

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