IPCCC Term DOUBLY COMMITTED JUXTA-ARTERIAL VENTRICULAR SEPTAL DEFECT WITHOUT MALALIGNMENT AND WITH PERIMEMBRANOUS EXTENSION
IPCCC Code 07.12.03
ICD-11 Code PENDING
IPCCC Definition A congenital cardiac malformation in which there is an outlet ventricular septal defect with perimembranous extension, bordered superiorly by the area of fibrous continuity or a fibrous outlet septum between the aortic and pulmonary valves, that is aligned with the trabecular muscular septum.
In this anterior view, the free wall of the right ventricle has been folded rightward to demonstrate doubly committed and juxta-arterial ventricular septal defect, bordered postero-inferiorly by fibrous continuity between the leaflets of tricuspid, aortic, and mitral valves. The defect opens to the outlet of the right ventricle between the limbs of the septal band and extends cranially to be bordered by an area of fibrous continuity (black dots) between the aortic and pulmonary valves. There is alignment between the fibrous outlet septum and the apical part of the muscular ventricular septum.
- Content for Echocardiogram
- Content for Computerized Axial Tomography
- Content for Angiography
- Content for Intraoperative Videos