06.05.25 – Double orifice of left ventricular component of common atrioventricular valve

IPCCC Term DOUBLE ORIFICE OF LEFT VENTRICULAR COMPONENT OF COMMON ATRIOVENTRICULAR VALVE

IPCCC Code 06.05.25

ICD-11 Code PENDING

Synonyms PENDING

Abbreviations PENDING

IPCCC Definition A congenital cardiac malformation in which the left ventricular component of the common atrioventricular valve has two orifices.

  • Image #1 shows a short axis view of the base of the heart as viewed from the atrial aspect. There is an unbalanced atrioventricular septal defect with right ventricular dominance and separate orifices for the right and left ventricles. The smaller left ventricular component itself exhibits a dual orifice. The smaller orifice extends along the postero-inferior aspect of the ventricular septum. In Image #2, the left ventricle has been opened in clamshell fashion, demonstrating the characteristic scooped-out crest (red dots) of the ventricular septum and the adherent inferior and superior bridging leaflets which separate the common atrioventricular junction into separate right and left ventricular orifices. Within the left component, the smaller orifice is supported by its own papillary muscle.
  • Content for Echocardiogram.
  • Content for Computerized Axial Tomography.
  • Content for Angiography.
  • Content for Intraoperative Videos.