07.12.03 – Doubly committed juxta-arterial ventricular septal defect without malalignment and with perimembranous extension

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IPCCC Term DOUBLY COMMITTED JUXTA-ARTERIAL VENTRICULAR SEPTAL DEFECT WITHOUT MALALIGNMENT AND WITH PERIMEMBRANOUS EXTENSION

IPCCC Code 07.12.03

ICD-11 Code PENDING

Synonyms PENDING

Abbreviations PENDING

IPCCC Definition A congenital cardiac malformation in which there is an outlet ventricular septal defect with perimembranous extension, bordered superiorly by the area of fibrous continuity or a fibrous outlet septum between the aortic and pulmonary valves, that is aligned with the trabecular muscular septum.

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07-12-03 In this anterior view, the free wall of the right ventricle has been folded rightward to demonstrate doubly committed and juxta-arterial ventricular septal defect, bordered postero-inferiorly by fibrous continuity between the leaflets of tricuspid, aortic, and mitral valves. The defect opens to the outlet of the right ventricle between the limbs of the septal band and extends cranially to be bordered by an area of fibrous continuity (black dots) between the aortic and pulmonary valves. There is alignment between the fibrous outlet septum and the apical part of the muscular ventricular septum.

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