07.11.16 – Muscular outlet ventricular septal defect with posteriorly malaligned outlet septum

IPCCC Term Muscular outlet ventricular septal defect with posteriorly malaligned outlet septumIPCCC Code 07.11.16ICD-11 Code PENDINGSynonyms PENDINGAbbreviations PENDINGIPCCC Definition A congenital cardiac malformation in which there is a ventricular septal defect that opens to the outlet of the right ventricle, with exclusively muscular borders when viewed from the right ventricle, and in which the muscular outlet septum is malaligned in postero-caudal fashion relative to the apical part of the muscular septum such that there is obstruction to the left ventricular outflow tract.

[/restabs

]