IPCCC Term Supravalvar or intravalvar mitral ring
IPCCC Code 05.02.02
ICD-11 Code PENDING
IPCCC Definition A congenital cardiac malformation in which a ridge of tissue is attached or integral to the atrial side of the mitral valvar leaflet(s).
Left Panel: This postero-superior view of the left atrioventricular junction shows a prominent, supravalvar ring (yellow dots) associated with the atrial aspect of the mitral valve. This ring is above the annulus or hinge point of the valve. Right Panel: The left atrioventricular junction is opened and viewed posteriorly, demonstrating a thickened mitral valve with thickened fused tendinous cords. Within the funnel of the mitral valve there is a prominent intravalvar ring (yellow dots).
- Content for Echocardiogram.
- Content for Computerized Axial Tomography.
- Content for Angiography.
- Content for Intraoperative Videos.