05.02.02 Supravalvar or intravalvar mitral ring

IPCCC Term Supravalvar or intravalvar mitral ring

IPCCC Code 05.02.02

ICD-11 Code PENDING

Synonyms PENDING

Abbreviations PENDING

IPCCC Definition A congenital cardiac malformation in which a ridge of tissue is attached or integral to the atrial side of the mitral valvar leaflet(s).

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Left Panel: This postero-superior view of the left atrioventricular junction shows a prominent, supravalvar ring (yellow dots) associated with the atrial aspect of the mitral valve. This ring is above the annulus or hinge point of the valve. Right Panel: The left atrioventricular junction is opened and viewed posteriorly, demonstrating a thickened mitral valve with thickened fused tendinous cords. Within the funnel of the mitral valve there is a prominent intravalvar ring (yellow dots).

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