01.01.16 – Partial anomalous pulmonary venous connection of Scimitar type

IPCCC Term PARTIAL ANOMALOUS PULMONARY VENOUS CONNECTION OF SCIMITAR TYPE

IPCCC Code 01.01.16

ICD-11 Code PENDING

Synonyms PENDING

Abbreviations PENDING

IPCCC Definition A congenital cardiovascular malformation with partial anomalous pulmonary venous connection in which some of the pulmonary veins (usually the right pulmonary veins) connect anomalously to the inferior caval vein (inferior vena cava) or to the right atrium at the insertion of the inferior vena cava.

  • This heart/lung block is obtained from a patient with Scimitar syndrome. Image # 1 shows the opened right atrium viewed from the front and slightly to the right. A probe has been placed in the solitary pulmonary vein draining the right lung, which opens anomalously into the inferior caval vein immediately above the diaphragm. Although not viewed in this image, the left pulmonary veins drained in the usual fashion to the left atrium.
  • Content for Echocardiogram.
  • Content for Computerized Axial Tomography.
  • Content for Angiography.
  • Content for Intraoperative Videos.
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