06.07.06-Atrioventricular septal defect with ventricular imbalance: dominant left ventricle, hypoplastic right ventricle

IPCCC Term Atrioventricular septal defect with ventricular imbalance: dominant left ventricle, hypoplastic right ventricle

IPCCC Code 06.07.06

ICD-11 Code PENDING

Synonyms PENDING

Abbreviations PENDING

IPCCC Definition A congenital cardiac malformation that is a variant of an atrioventricular septal defect (atrioventricular canal defect) with the left ventricle significantly larger than the right.

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This heart has been sectioned to demonstrate the short axis of the ventricular mass. It is photographed to show the view from the apex looking towards the base. There is an atrioventricular septal defect with a common atrioventricular junction. The common atrioventricular valve is committed predominately to the left ventricle, resulting on left ventricular dominance. The papillary muscles (black stars) are close together within the left ventricle, which shows excessive trabeculations. The zone of apposition between the superior and inferior bridging leaflets is marked with the yellow lines. The right ventricular cavity is hypoplastic as is the right component of the common atrioventricular valve.

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