04.04.14 – Coronary sinus orifice atresia or stenosis

IPCCC Term CORONARY SINUS ORIFICE ATRESIA OR STENOSIS

IPCCC Code 04.04.14

ICD-11 Code PENDING

Synonyms PENDING

Abbreviations PENDING

IPCCC Definition A congenital cardiac malformation in which the orifice of the coronary sinus is narrowed or absent.

  • Image #1 shows an anterior view of the right atrioventricular junction in a heart with double inlet left ventricle and atresia of the coronary sinus (yellow brackets). The Eustachian valve is marked with red dots and there is a small deficiency in the flap valve or atrial septal defect at the floor of the oval fossa. The same heart is depicted from behind in Image #2 with a small vertical vein draining the coronary veins that were attached to the obstructed coronary sinus. This vertical vein is in the same position as a persistent left superior caval vein and drains the coronary venous blood to the left brachiocephalic vein.
  • Content for Echocardiogram.
  • Content for Computerized Axial Tomography.
  • Content for Angiography.
  • Content for Intraoperative Videos.