IPCCC Term ATRIOVENTRICULAR SEPTAL DEFECT AND TETRALOGY OF FALLOT (ATRIOVENTRICULAR CANAL AND TETRALOGY OF FALLOT)
IPCCC Code 01.01.20
ICD-11 Code PENDING
IPCCC Definition A congenital cardiac malformation with both an atrioventricular septal defect (atrioventricular canal defect) and tetralogy of Fallot.[restabs alignment=”osc-tabs-right” pills=”nav-pills” responsive=”true” icon=”true” text=”More”][restab title=”Anatomic Specimen” active=”active”]
|This heart is viewed in an anterior anatomic position and has been sectioned to illustrate the left and right ventricular outflow tracts and common atrioventricular valve. The specimen is photographed from the front, simulating the subcostal long-axis echocardiographic plane. There is antero-cephalad deviation of the outlet septum producing severe subpulmonary infundibular and valvar stenosis. The aortic valve overrides the interventricular septum in this heart with tetralogy of Fallot. There is also an atrioventricular septal defect with a common atrioventricular junction and valve.