IPCCC: 07.08.50, 03.01.05 [01.03.03], 01.04.01, 01.05.01
 

AEPC Derived Term:    

Ventricular myocardial noncompaction cardiomyopathy (07.08.50)

Left isomerism ('polysplenia') (03.01.05) vs

Isomerism of left atrial appendages (left isomerism) (01.03.03)

Discordant AV connections (01.04.01)
Discordant VA connections (TGA) (01.05.01)

EACTS-STS Derived Term:    

Cardiomyopathy, Spongiform cardiomyopathy (Noncompaction cardiomyopathy) (Embryonal cardiomyopathy) (07.08.50)

Atrial appendage isomerism, Left (03.01.05) vs

Syndrome, Heterotaxy (heterotaxy syndrome) (visceral heterotaxy)-modifier, Isomerism, Isomerism of the left atrial appendages

AV connection(s) = Discordant AV connections (biventricular) (01.04.01)

VA connection =Discordant VA connections (TGA) (01.05.01)

Definition:  pending

Common Synonyms:  pending

Modality: Anatomic specimen

Orientation: Short axis - apical view

Description: This apical view of the ventricles demonstrates biventricular, spongiform myocardium or so-called non-compaction.  There is a subendocardial, compact zone with a highly trabeculated inner myocardial component.  The atrioventricular connections are discordant in this heart with isomerism of the left atrial appendages, ventricular inversion and left-hand ventricular topology.  There are discordant ventriculo-arterial connections, the aorta arising from the left-sided morphologically right ventricle above a subaortic infundibulum (yellow asterisk).

Contributor: Diane E. Spicer, BS

Institution: The Congenital Heart Institute of Florida (CHIF)

Image Label: A070850-80a

Source of Image: Van Mierop Archive, University of Florida

Image Certification: pending

AWG Rating: pending

Modality: Anatomic specimen

Orientation: Short axis - apical view

Description: This view illustrates the apical trabecular pattern of both ventricles allowing for morphologic differentiation in this heart with spongiform myocardium.  The left-sided, coarsely trabeculated ventricle is consistent with a morphologically right ventricle, while the right-sided ventricle has fine apical trabeculations, consistent with a morphologically left ventricle.  The subendocardial compact zone is shown between the epicardium and the red dots, the highly trabeculated myocardium closely related to the ventricular cavity and more prominent within the left ventricle. 

Contributor: Diane  E. Spicer, BS

Institution: The Congenital Heart Institute of Florida (CHIF)

Image Label: A070850-80b

Source of Image: Van Mierop Archive, University of Florida

Image Certification: pending

AWG Rating: pending

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