IPCCC Code: 01.01.03, 01.03.00, 07.10.00, 07.09.01
 

AEPC Code:    

Congenitally corrected transposition of great arteries (discordant AV & VA connections), Usual atrial arrangement (atrial situs solitus), VSD, Left ventricular outflow tract obstruction

EACTS-STS Code:    

Discordant AV connections with situs solitus, Discordant VA connection (Congenitally corrected transposition) (usually {SLL}), VSD and LVOTO

Definition:  NA

Common Synonyms: NA

Discussion:  Anatomic views of the right and left sides of the heart demonstrate the discordant atrioventricular connections associated with congenitally corrected transposition. There is a muscular ventricular septal defect (VSD). The percentage of hearts with ventricular septal defects is approximately the same when comparing hearts with discordant atrioventricular and ventriculoarterial connections to those hearts with concordant connections.

The superior (SCV) and inferior (ICV) caval veins drain into the morphologically right atrium (mRA) on the right side of the heart, in the normal fashion. The morphologically right atrium is connected to the morphologically left ventricle (mLV) on the right side of the heart with the mitral valve (MV) in the inlet component. (OF-oval fossa, CS-coronary sinus)

Contributor: Diane Spicer, BS

Image Name: CTGA2a.jpg

Close up view of the same heart seen in view 2a, demonstrating the muscular ventricular septal defect (VSD)

Contributor: Diane Spicer, BS

Image Name: CTGA2a1.jpg

The tricuspid valve (TV) guards the inlet of this left-sided morphologically right ventricle (mRV). The aorta (Ao) is connected to the left-sided morphologically right ventricle, the arterial valve separated from the atrioventricular valve by the infundibulum. (mLA-morphologically left atrium, VSD-ventricular septal defect)

Contributor: Diane Spicer, BS

Image Name: CTGA2b.jpg

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