IPCCC Code: 01.01.03, 01.03.00, 06.01.75
 

AEPC Code:    

Congenitally corrected transposition of great arteries (discordant AV & VA connections), Usual atrial arrangement (atrial situs solitus), Ebstein's malformation of 'left-sided' tricuspid valve in discordant atrioventricular connections

EACTS-STS Code:    

Discordant AV connections with situs solitus, Discordant VA connection (Congenitally corrected transposition) (usually {SLL}), Tricuspid valve disease, Ebstein's anomaly, "Left-sided" Ebstein's anomaly (Ebstein's malformation of 'left-sided' tricuspid valve in discordant atrioventricular connections)

Definition:  NA

Common Synonyms: NA

This view of the right-sided morphologically left ventricle (mLV) shows the mitral valve (MV) in the inlet portion. Not shown is the discordant connection between the morphologically right atrium and the morphologically left ventricle. The pulmonary trunk (PT) is in the outlet portion, demonstrating the discordant ventriculoarterial connection on the right side. Note the fibrous continuity between the mitral valve and the pulmonic valve.  The aorta is in its usual left-sided location relative to the pulmonary trunk in a heart with congenitally corrected transposition. (LPA-left pulmonary artery, RPA- right pulmonary artery)

Contributor: Diane Spicer, BS

Image Name: CTGA3a.jpg

This anatomic view of the left side of the heart with congenitally corrected transposition demonstrates the discordant atrioventricular connection. The morphologically left atrium (mLA) is connected to the morphologically right ventricle (mRV) on the left side of the heart with the tricuspid valve (TV) in the inlet portion. The left-sided, morphologically tricuspid valve exhibits an Ebstein malformation (arrows) that is sometimes associated with congenitally corrected transposition. There is atrialization of the left-sided morphologically right ventricle. (OF-oval fossa)

Contributor: Diane Spicer, BS

Image Name: CTGA3b.jpg

The outlet portion of the left-sided morphologically right ventricle (mRV) supports the aorta. Note the muscular infundibulum separating the artrioventricular valve from the arterial valve. (mLAA- morphologically left atrial appendage, TV-tricuspid valve)

Contributor: Diane Spicer, BS

Image Name: CTGA3c.jpg

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