IPCCC Code: 07.15.04, 07.11.05, 07.10.01, 07.13.05, 01.01.18
 

AEPC Derived Term:    

Multiple VSDs (07.15.04)

Muscular VSD: multiple trabecular (Swiss cheese) (07.11.05)

Perimembranous VSD (07.10.01)

VSD in double outlet VA connection: subpulmonary (07.13.05)

Double outlet right ventricle: transposition type (subpulmonary VSD) (01.01.18)

EACTS-STS Derived Term:   

VSD, Multiple (07.15.04)

VSD, Type 4 (Muscular), Multiple - "Swiss-Cheese" (07.11.05)

VSD, Type 2 (Perimembranous) (Paramembranous) (Conoventricular) (07.10.01)

VA connection =Double outlet VA connections-modifier for VSD in double outlet VA connection, Subpulmonary (07.13.05)

DORV, "TGA type" (Subpulmonary VSD) (01.01.18)

Definitions: 

Commentary:

Common Synonyms:

• 07.11.05: Multiple (more than 3) muscular VSDs

• 07.10.01: A ventricular septal defect contiguous with the site of the membranous septum. The membranous septum is defined as the area of the septum contiguous with the fibrous continuity between the leaflets of an atrioventricular valve and an arterial valve

• 07.13.05: A VSD in the setting of double outlet ventricle located directly beneath the pulmonary valve and is remote from the aortic valve

• 07.15.04: The presence of multiple holes between the ventricles

• 07.11.05: It is desirable to specify the number of orifices from both the left ventricular and right ventricular aspects

• 07.10.01: This is a generic term that, if possible, should be qualified by more specific terms regarding extension. This term is used by some to include conoventricular VSD, paramembranous VSD, type II VSD, inlet VSD and atrioventricular canal VSD. This term is used by some to describe an isolated perimembranous VSD without extension or a conoventricular VSD without malalignment. These defects have part of their margins made up of fibrous continuity either between the leaflets of an atrioventricular and an arterial valve or, in the setting of double outlet right ventricle or overriding of the tricuspid valve, by fibrous continuity between the leaflets of the mitral and tricuspid valves. Such defects can extend to become doubly committed and juxtaarterial when there is also fibrous continuity between the leaflets of the arterial valve or when there is a common arterial valve
   

          NA

Modality: Anatomic specimen

Orientation: Anterior view of the right ventricle

Description:  The outlet components and septal surface of this heart with double outlet right ventricle are viewed from the apex. The aorta (A) is anterior and to the right of the pulmonary trunk (PT). The aortic valve (AV) is supported by a complete muscular infundibulum and the pulmonary valve (PV) lies above a perimembranous ventricular septal defect (PMVSD). The tricuspid valve (TV) guards the inlet of this morphologically right ventricle and is in fibrous continuity with the pulmonary valve. At the apex there are multiple, muscular ventricular septal defects (MVSD).

Contributor: Diane Spicer, BS

Institution: The Congenital Heart Institute of Florida (CHIF)

Image Label: A071504-53a

Source of Image:  Van Mierop Archive, University of Florida, Gainesville, FL

Image Certification: pending

AWG Rating:

Modality: Anatomic specimen

Orientation: Left ventricular view

Description: The left ventricle of the heart shown in the left panel is opened in a clam-shell fashion demonstrating the perimembranous ventricular septal defect (PMVSD) and the multiple, apical, muscular ventricular septal defects (MVSD). The mitral valve (MV) guards the inlet of this morphologically left ventricle. (LAA-left atrial appendage)

Contributor: Diane Spicer, BS

Institution: The Congenital Heart Institute of Florida (CHIF)

Image Label: A071504-53b

Source of Image:  Van Mierop Archive, University of Florida, Gainesville, FL

Image Certification: pending

AWG Rating:

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