TAPVC, Supracardiac: IPCCC Code: 04.06.00, 04.06.03, Q1.01.51

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Paediatric and Congenital Heart Disease

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IPCCC: 04.06.00, 04.06.03, Q1.01.51
	AEPC Derived Term:	Totally anomalous pulmonary venous connection: supracardiac (04.06.00) Supracardiac location of anomalous pulmonary venous connection(s) to left-sided vertical vein - all pulmonary veins (04.06.03, Q1.01.51)

	EACTS-STS Derived Term:	Total anomalous pulmonary venous connection (TAPVC), Type 1 (supracardiac) (04.06.00) Pulmonary venous connection anomalous, Supracardiac-modifier for site of drainage, Supracardiac location of APVC to left-sided vertical vein, All pulmonary veins (04.06.03, Q1.01.51)

	ICD 10 Term:	Total anomalous pulmonary venous connection (Q26.2)

Definition: pending

Common Synonyms: pending

	Modality: Anatomic specimen Orientation: Anterior view Description: The anterior anatomic view in this heart with concordant atrioventricular and ventriculo-arterial connections demonstrates a normally related aorta and pulmonary trunk (PT). The left brachiocephalic vein (LBCV) drains normally to the superior caval vein, and the azygos vein has been lifted from its usual position to extend the superior caval vein. There is supracardiac totally anomalous pulmonary venous return via a vertical vein (red arrow) to the left brachiocephalic vein. The right and left pulmonary veins join in a confluence (see image A040600-124b) posterior to the heart, the vertical vein then extending posterior to the arterial duct. (yellow asterisk- right pulmonary artery, LCCA-left common carotid artery, LPA-left pulmonary artery, RCCA-right common carotid artery) Contributor: Diane E. Spicer, BS Institution: The Congenital Heart Institute of Florida (CHIF) Image Label: A040600-124a Source of Image: Idriss Archive, Children’s Memorial Hospital, Chicago, IL Image Certification: pending AWG Rating: pending	Modality: Anatomic specimen Orientation: Posterior inferior view Description: The heart has been lifted cephalad, using the so-called Taussig maneuver (reference below), to demonstrate the confluence between the right and left pulmonary veins, which is posterior to the heart. A vertical vein (red arrow) then extends from the confluence, running between the pulmonary arteries and the left bronchus, the so-called bronchopulmonary vice, before draining into the left brachiocephalic vein (see image A040600-124a). (Blue asterisk- left main bronchus) Contributor: Diane E. Spicer, BS Institution: The Congenital Heart Institute of Florida (CHIF) Image Label: A040600-124b Source of Image: Idriss Archive, Children’s Memorial Hospital, Chicago, IL Image Certification: pending AWG Rating: pending

In Pediatric Autopsy: Fetus, Newborn and Child (Ch 2). Editors: Enid Gilbert-Barness and Diane E. Debich-Spicer. Handbook of Pediatric Autopsy Pathology. 1st ed. Totowa, NJ: Humana Press;2005:17

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