Images & Codes 

 

Archiving Working Group

International Society for Nomenclature of

Paediatric and Congenital Heart Disease

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IPCCC: 07.09.00, 09.15.22, 07.10.00
 

 

AEPC Derived Term:    

Subaortic stenosis (07.09.00)
Bicuspid aortic valve (09.15.22)
Ventricular septal defect (VSD) (07.10.00)

 
       
 

EACTS-STS Derived Term:    

Aortic stenosis, Subvalvar (07.09.00)
Aortic valve pathology, Bicuspid (09.15.22)
VSD (07.10.00)

 
       
 

ICD 10 Term:     

Congenital subaortic stenosis (Q24.4)
Bicuspid aortic valve(Q23.1)
Ventricular septal defect (Q21.0)

 
       
 

Definition:  pending


Common Synonyms:  pending

 

 

 

 

 

Modality: Anatomic specimen

Orientation: Outflow tract view from left ventricular apex

Description: Looking up the aortic outflow from the apex of the left ventricle, there is a well circumscribed subaortic fibrous ring (SAR) causing severe subaortic stenosis. This ring is just inferior to the aortic valve leaflets and extends through the area where the anterior leaflet of the mitral valve (MV) and aortic valve are in fibrous continuity. There is a ventricular septal defect (VSD), that had been previously surgically repaired, inferior to the subaortic fibrous ring. The patch on the right ventricular surface covering the ventricular septal defect orifice is not visualized.
Contributor: Diane E. Spicer, BS

Institution: The Congenital Heart Institute of Florida (CHIF)

Image Label: A070900-24a

Source of Image: Van Mierop Archive, University of Florida, Gainesville, Florida

Image Certification:

AWG Rating: 5 January 2013    

 

 

 

 

Modality: Anatomic specimen

Orientation: Opened left ventricular outflow tract view

Description: The subaortic fibrous ring (yellow dots) and left ventricular outflow tract have been opened, using a single cut, demonstrating the severe subaortic stenosis. It extends through the area where the anterior leaflet of the mitral valve and the aortic valve are in fibrous continuity. The aortic valve (AoV) is thickened and is bicuspid. Note the high take off of the right coronary orifice (RCO). The left coronary orifice (LCO) and left main coronary artery have been transected. (VSD-ventricular septal defect).

Contributor: Diane E. Spicer, BS

Institution: The Congenital Heart Institute of Florida (CHIF)

Image Label: A070900-24b

Source of Image: Van Mierop Archive, University of Florida, Gainesville, Florida

Image Certification:

AWG Rating: 5 January 2013

 
         
 

 

 

Modality: Three dimensional echocardiogram

Orientation:Three dimensional parasternal short axis image

Description: This 3D echo videoclip in the parasternal short-axis orientation is from a different patient with a subaortic fibrous ring (SAR). Note the striking similarity between the gross specimen above and this 3D image. The SAR in the left ventricular outflow tract is seen best between 4 and 9 o'clock in this orientation. The aortic valve leaflets are not seen in this view. The atrial septum is seen at approximately 7 o'clock and the septal leaflet of the tricuspid valve is seen opening and closing at approximately 10 o'clock.

Contributor: Javier González González, MD

Institution: The Congenital Heart Institute of Florida (CHIF)

Image Label: E070900-24c

Source of Image: The Congenital Heart Institute of Florida (CHIF)

Image Certification: 5 January 2013

AWG Rating:

 
     
 

AWG Page Certification: 5 January 2013  

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