Aortic Arch Interruption (Type B) & Single Ventricle, Double Inlet: IPCCC Code: 09.29.33, 01.04.04, 01.03.00, 02.03.01, 02.06.02, 07.02.00, 07.10.00, 01.05.01

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IPCCC: 09.29.33, 01.04.04, 01.03.00, 02.03.01, 02.06.02, 07.02.00, 07.10.00, 01.05.01
	AEPC Derived Term:	Interrupted aortic arch between subclavian & common carotid arteries (type B) (09.29.33) Double inlet left ventricle (01.04.04) Usual atrial arrangement (atrial situs solitus) (01.03.00) Right hand pattern ventricular topology (02.03.01) Aortic orifice anterior right with respect to pulmonary orifice (02.06.02) Right ventricular hypoplasia (07.02.00) VSD (07.10.00) Discordant VA connections (TGA) (01.05.01)

	EACTS-STS Derived Term:	Interrupted aortic arch (IAA), Type B (Interruption between the carotid and subclavian arteries) (09.29.33) Single ventricle, DILV, {SDD}, Subaortic RV outlet chamber with VSD (Bulboventricular foramen) (01.04.04, 01.03.00, 02.03.01, 02.06.02, 07.02.00, 07.10.00, 01.05.01)

	ICD-10 Derived Term:	Other congenital malformations of aorta (Q25.4) Double inlet ventricle (Q20.4)

Definition: pending

Common Synonyms: pending

Modality: Anatomic specimen

Orientation: Anterior view

Description: This external view of the great arteries is viewed from the anterior, left side, illustrating an interrupted aortic arch. The aorta is interrupted between the left common carotid (LCCA) and the left subclavian (LSA) arteries. The left subclavian artery arises from the descending aorta (DAo) quite a distance from where the patent arterial duct (PAD) joins the aorta. The anterior aspect of the right and left ventricles have been obliquely resected in this heart with double inlet left ventricle (not shown), exposing the rudimentary right ventricle (RudRV), with the aorta (A) arising from it. The apical trabecular portion of the left ventricle (LV) and the interventricular septum (IVS) is seen. (LAA-left atrial appendage, PT-pulmonary trunk, RAA-right atrial appendage, RCCA-right common carotid, RSA-right subclavian artery, SCV-superior caval vein)

Contributor: Diane Spicer, BS

Institution: The Congenital Heart Institute of Florida (CHIF)

Image Label: A010404-19a

Source of Image: Van Mierop Archive, University of Florida, Gainesville, Florida

Image Certification: 5 Nov 2011

AWG Rating:

AWG Page Certification: 5 Nov 2011