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Position and connection of heart |
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Position-orientation of heart abnormal |
Dextrocardia: heart predominantly in R hemithorax |
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Position or morphology of thoraco-abdominal organs abnormal |
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Abnormal atrial arrangement |
Total mirror imagery (atrial situs inversus) |
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Right isomerism ('asplenia') |
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Left isomerism ('polysplenia') |
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AV and/or VA connections abnormal |
Double inlet ventricle |
Double inlet RV |
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Double inlet LV |
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Tricuspid atresia |
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Mitral atresia |
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Solitary ventricle of indeterminate morphology |
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Congenitally corrected transposition of great arteries |
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Discordant VA connections (TGA) |
Complete transposition of great arteries (IVS) |
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Congenitally corrected transposition of great arteries |
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Double outlet RV |
Double outlet RV - Fallot type |
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Double outlet RV - transposition type |
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Double outlet RV - with non-committed VSD |
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Double outlet LV |
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Common arterial trunk |
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Great veins |
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Superior caval vein (SVC) abnormality |
Left SVC persisting to coronary sinus |
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Inferior caval vein (IVC) abnormality |
Azygous continuation of IVC |
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Hepatic vein abnormality |
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Systemic vein abnormality - congenital |
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Pulmonary vein abnormality |
Pulmonary vein stenosis |
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Totally anomalous pulmonary venous connection |
Totally anomalous pulmonary venous connection - supracardiac |
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Totally anomalous pulmonary venous connection - intracardiac |
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Totally anomalous pulmonary venous connection - infracardiac |
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Totally anomalous pulmonary venous connection - mixed |
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Partially anomalous pulmonary venous connection(s) |
Partially anomalous pulmonary venous connections: Scimitar |
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Coronary sinus abnormality |
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Atriums and atrial septum |
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RA abnormality |
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LA abnormality |
Cor triatriatum (divided left atrium) |
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Intact atrial septum |
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Atrial septum abnormality |
Patent foramen ovale (PFO) |
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ASD |
ASD within oval fossa (secundum) |
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Sinus venosus ASD |
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Common atrium (virtual absence of atrial septum) |
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Interatrial communication (ASD) through coronary sinus orifice |
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AV valves and AV septal defect |
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Tricuspid valvar abnormality |
Tricuspid regurgitation |
Tricuspid regurgitation - congenital |
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Tricuspid valvar dysplasia (mucoid thickening) |
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Straddling tricuspid valve |
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Ebstein's malformation of tricuspid valve |
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Tricuspid stenosis |
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Mitral stenosis |
Mitral valve stenosis |
Mitral valvar stenosis - congenital |
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Mitral subvalvar stenosis |
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Supravalvar mitral ring |
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Mitral valvar abnormality |
Mitral regurgitation |
Mitral regurgitation - congenital |
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Mitral valve stenosis |
Mitral valvar stenosis - congenital |
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Straddling mitral valve |
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Supravalvar mitral ring |
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Mitral valvar prolapse |
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True cleft of mitral valve |
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Mitral subvalvar apparatus abnormality |
Mitral subvalvar stenosis |
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Parachute malformation of mitral valve |
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Atrioventricular septal defect |
AVSD: isolated atrial component (primum ASD) |
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AVSD: isolated ventricular component |
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AVSD: atrial & ventricular components (complete) |
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AVSD: atrial & ventricular components + separate AV valves
('intermediate') |
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AVSD with ventricular imbalance |
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AVSD AV valvar abnormality |
AVSD AV valvar regurgitation |
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AV septal defect and Tetralogy of Fallot |
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Ventricles and ventricular septum |
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Functionally univentricular heart |
Ventricular imbalance: dominant LV + hypoplastic RV |
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Ventricular imbalance: dominant RV + hypoplastic LV |
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RV abnormality |
RV aneurysm |
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RV hypoplasia |
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Double chambered RV |
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RV outflow tract obstruction |
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LV abnormality |
LV hypoplasia |
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LV aneurysm |
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Hypoplastic left heart syndrome |
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LV outflow tract obstruction |
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Intact ventricular septum |
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Ventricular septal abnormality |
VSD |
Tiny VSD (Maladie de Roger) |
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Single VSD |
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Multiple VSDs |
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Perimembranous VSD |
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VSD + malaligned outlet septum |
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Inlet VSD |
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Muscular VSD |
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Subarterial VSD |
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Communication between LV-RA (Gerbode defect) |
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Spontaneous closure of VSD |
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Aneurysm of membranous septum |
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VA valves and great arteries |
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Aortopulmonary window |
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Pulmonary artery from ascending aorta (hemitruncus) |
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Truncal valvar abnormality |
Truncal valvar regurgitation |
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Pulmonary stenosis |
Subpulmonary stenosis |
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Pulmonary valvar stenosis |
Pulmonary valvar stenosis - congenital |
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Supravalvar pulmonary trunk stenosis |
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Pulmonary valvar abnormality |
Pulmonary valvar stenosis |
Pulmonary valvar stenosis - congenital |
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Pulmonary regurgitation |
Pulmonary regurgitation - congenital |
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Pulmonary atresia |
Pulmonary atresia - imperforate valve |
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Pulmonary atresia + intact ventricular septum |
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Coronary fistulas from RV ('sinusoidal') |
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RV dependent coronary circulation |
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Pulmonary trunk (MPA) abnormality |
Supravalvar pulmonary trunk stenosis |
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Pulmonary trunk hypoplasia |
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Pulmonary arterial abnormality |
Pulmonary arterial stenosis |
Central pulmonary arterial stenosis - proximal to hilar bifurcation |
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Peripheral pulmonary arterial stenoses - at/beyond hilar bifurcation |
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Pulmonary arterial hypoplasia |
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Discontinuous (non-confluent) pulmonary arteries |
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Pulmonary arterial aneurysm |
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Aortic stenosis |
Subaortic stenosis |
Subaortic stenosis due to fibromuscular shelf |
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Aortic valvar stenosis |
Aortic valvar stenosis - congenital |
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Supravalvar aortic stenosis |
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Aortic valvar abnormality |
Aortic valvar stenosis |
Aortic valvar stenosis - congenital |
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Eccentric opening of tricuspid aortic valve |
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Aortic regurgitation |
Aortic regurgitation - congenital |
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Bicuspid aortic valve |
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Aortic valvar atresia |
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Aortic valvar prolapse |
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Ascending aorta abnormality |
Ascending aorta hypoplasia |
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Supravalvar aortic stenosis |
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Ascending aorta dilation |
Ascending aorta dilation associated with Marfan syndrome |
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Aortic sinus of Valsalva aneurysm |
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Aorto-LV tunnel |
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Aortic arch abnormality |
Right aortic arch |
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Aortic coarctation |
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Aortic arch hypoplasia (tubular) |
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Interrupted aortic arch |
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Aortic arch branch abnormality |
Aberrant origin R subclavian artery |
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Vascular ring |
Double aortic arch |
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Pulmonary arterial sling |
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Descending aorta dilation |
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Descending/ abdominal aorta hypoplasia |
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Coronary arteries/Arterial duct |
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Pericardium/AV fistulae |
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Coronary arterial abnormality |
Anomalous origin of coronary artery from pulmonary artery |
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Coronary fistula |
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Coronary artery: anomalous aortic origin / course |
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Coronary arterial aneurysm(s) |
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Arterial duct (ductus arteriosus) abnormality |
Patent arterial duct (PDA) |
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Arteriovenous fistula |
Pulmonary arteriovenous fistula |
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Distal systemic arterial abnormality |
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Pericardial abnormality |
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Tetralogy of Fallot and variants |
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Tetralogy of Fallot |
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Pulmonary atresia + VSD (including Fallot type) |
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Pulmonary atresia + VSD + 'MAPCA'(s) |
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Absent pulmonary valve syndrome - Fallot-type |
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Solitary arterial trunk (absent intrapericardial PAs) |
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Major systemic-to-pulmonary collateral artery (MAPCA) |
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